• | AKA Senear-Usher syndrome |
• | overlap features of both diseases: |
• | butterfly rash, photosensitivity/ trunk lesions similar to pemphigus foliaceus |
◆ | granular IgG and C3 at the basement membrane zone/ intercellular IgG and C3 in epidermis |
• | ANA+ but rarely progresses to systemic LE |
• | may be associated with myasthenia gravis |
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