| • | incontinentia pigmenti – peg teeth |
| • | Papillon Lefevre - periodontosis The primary (deciduous) teeth frequently become loose and fall out by about age five. Without treatment, most of the secondary (permanent) teeth may also be lost by approximately age 17 |
| • | tuberous sclerosus – enamel pits (100%) |
| • | anhidrotic ectodermal dysplasia - abnormal morphogenesis or absence of teeth may occur |
| • | pachyonychia congenita type II - natal teeth |
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